Etiology

Autosomal dominant

Predilection

Location

Mandible

Maxilla

Skin

Clinical Appearance

Multiple odontogenic, keratocysts and basal cell carcinoma

Radiographic Features

Multiple radiolucencies in both maxilla and mandible

Bifid rib

Microscopic Features

Same as carcinomas

Treatment

Surgical removal cysts and basal cell carcinoma

Diagnostic Process

Clinical

Radiographic

Family History

Photos Gallery

Photo 1