Etiology

Unknown

Theory=abnormal mesencymal cell function

Predilection

Children and young adults

Location

Monostatic=one bone

Greater in the maxilla

Frequently affected bones, rubs, femur, tibia

Polystatic/Jaffe type

Clinical Appearance

Oral/facial painless swelling of the jaw

Malocclusion

Displacement of teeth

Cafe` a Lait macules on skin

Polystatic/Jaffe type=more than one bone involved

Albright syndrome=Extensive, progressive involvement of many bones

Endocrine abnormalities

Radiographic Features

Diffuse "ground glass" radioluceny

Abnormal bone blends into normal bone

Unilocular and multilocular radiolucencies

Microscopic Features

Benign fibro-ossious lesions

Treatment

Surgical recontouring of bone for cosmetic reasons

Diagnostic Process

Radiographic

Microscopic

Photos Gallery

Monostatic Dysplasia
Photo 1
Photo 2 Photo 3

Polyostatic Fibrous Dysplasia
Photo 1

Cafe` a Lait Spots
Photo 1

Albright Syndrome
Photo 1